Illnesses of a pancreas. Kistoznyj fibroz a pancreas

you in section: Illnesses of a pancreas

Disease is described for the first time in 1905 K Landsteiner, D. Fancni (1925-1933) and D. H. Andersen (1932) have established that this congenital pathology is usually combined with defeat of bronchial tubes, lungs and a liver. At the heart of illness lies fermentativnyj defect of a mucous secret endokrinnyh glands that leads to accumulation in a gleam of bronchial tubes, tracheas, pancreas channels, sometimes in guts of the dense, viscous mucous or mucopurulent weights corking channels, in this connection above a place obturatsiiobrazujutsja kisty round which then the fibrous fabric develops. A consequence of all of it is functional inferiority first of all a pancreas, shown by diarrheas which are considered as idiopaticheskaja a diarrhoeia with steatoreej. The following on frequency a place is occupied with a pathology bronholegochnogo the device in the form of a persistent bronchitis, a pneumonia, bronhoektazov with the subsequent development of pulmonary heart.

Now pancreatic kistoz it is considered as sistemnoenasledstvennoe the disease transferred on autosomno-retsessivnomu to type and characterised sochetannym by defeat of a pancreas and bronholegochnogo of the device. Its most accepted name - mukovistsidoz (S. Farber, 1944; M.I.Rejderman, 1974).

Disease is quite often found out in the first months of a life of the child by the phenomena so-called mekonievoj impassability, sometimes it comes to light at the age of 1-3 has laid down and is accompanied by a sharp delay of the general development.